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AlternativeComplement Pathway Regulation Atypical HUS (aHUS) occurs due to endothelial damage following abnormal complement regulation, with some cases being deficient in complement regulating factors H, I and Membrane Cofactor P. © Wilkinson H, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hannah Wilkinson* John Dixon and Fiona Harris aHUS: Atypical HUS ANA: Antinuclear Antibody ANCA: Anti-neutrophil Cytoplasmic Antibodies D+ HUS: HUS withDiarrhoea D-HUS: HUS without Diarrhoea LDH: Lactate Dehydrogenase MCP: Membrane Cofactor Protein RBC: Red Blood cells RCA:Regulators of Complement Activation 2016-06-04T18:32:02+05:30 2016-06-04T18:32:02+05:30 2016-06-04T18:32:02+05:30 5 Adobe InDesign CS6 (Windows) uuid:aa0675ce-ec4f-4cc6-a096-38c5726e45ba xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 xmp.id:40B7023F502AE61184C9F4E5272ACB33 proof:pdf xmp.iid:3FB7023F502AE61184C9F4E5272ACB33 xmp.did:F2BC7D9EC6C7E411AEB789ACBE3823B3 xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 default converted from application/x-indesign to application/pdf Adobe InDesign CS6 (Windows) / 2016-06-04T18:32:02+05:30 Citation: Wilkinson H, Dixon J, Harris F (2016) CaseReport: Atypical Haemolytic Uraemic SyndromeDue to Abnormal Alternative Complement PathwayRegulation. doi http://dx.doi.org/10.16966/2380-5498.131 Hannah Wilkinson, Nephrology Department, St. Helier Hospital, WrytheLane, Carshalton, Surrey, United Kingdom, Tel: 07967791995; E-mail: hannah.wilkinson@esth.nhs.uk Adobe PDF Library 10.0.1 False endstream endobj 147 0 obj <> endobj xref 0 654 0000000000 65535 f 0000248798 00000 n 0000249233 00000 n 0000249257 00000 n 0000258717 00000 n 0000258776 00000 n 0000259225 00000 n 0000259486 00000 n 0000259620 00000 n 0000263987 00000 n 0000264071 00000 n 0000264131 00000 n 0000264216 00000 n 0000264827 00000 n 0000265189 00000 n 0000265526 00000 n 0000266800 00000 n 0000282428 00000 n 0000282504 00000 n 0000283037 00000 n 0000283113 00000 n 0000283150 00000 n 0000319974 00000 n 0000320344 00000 n 0000320685 00000 n 0000320800 00000 n 0000320863 00000 n 0000321176 00000 n 0000321652 00000 n 0000321769 00000 n 0000321832 00000 n 0000322111 00000 n 0000322300 00000 n 0000322376 00000 n 0000322453 00000 n 0000322475 00000 n 0000322551 00000 n 0000322628 00000 n 0000322650 00000 n 0000322802 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regulation, with some cases being deficient in complement regulating factors H, I and Membrane Cofactor P. © Wilkinson H, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Hannah Wilkinson* John Dixon and Fiona Harris aHUS: Atypical HUS ANA: Antinuclear Antibody ANCA: Anti-neutrophil Cytoplasmic Antibodies D+ HUS: HUS withDiarrhoea D-HUS: HUS without Diarrhoea LDH: Lactate Dehydrogenase MCP: Membrane Cofactor Protein RBC: Red Blood cells RCA:Regulators of Complement Activation 2016-06-04T18:32:02+05:30 2016-06-04T18:32:06+05:30 2016-06-04T18:32:06+05:30 5 Adobe InDesign CS6 (Windows) uuid:800759a9-60a3-4233-8f9c-ff826fb4699f xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 xmp.id:40B7023F502AE61184C9F4E5272ACB33 proof:pdf xmp.iid:3FB7023F502AE61184C9F4E5272ACB33 xmp.did:F2BC7D9EC6C7E411AEB789ACBE3823B3 xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 default converted from application/x-indesign to application/pdf Adobe InDesign CS6 (Windows) / 2016-06-04T18:32:02+05:30 Citation: Wilkinson H, Dixon J, Harris F (2016) CaseReport: Atypical Haemolytic Uraemic SyndromeDue to Abnormal Alternative Complement PathwayRegulation. doi http://dx.doi.org/10.16966/2380-5498.131 Hannah Wilkinson, Nephrology Department, St. Helier Hospital, WrytheLane, Carshalton, Surrey, United Kingdom, Tel: 07967791995; E-mail: hannah.wilkinson@esth.nhs.uk Adobe PDF Library 10.0.1 False endstream endobj 147 0 obj <> endobj 655 0 obj <>/Metadata 146 0 R/Names 656 0 R/Outlines 107 0 R/PageMode/UseOutlines/Pages 145 0 R/StructTreeRoot 148 0 R/Type/Catalog/ViewerPreferences<>>> endobj xref 0 1 0000000000 65535 f 146 2 0000362677 00000 n 0000369703 00000 n 655 1 0000370226 00000 n trailer <]/Prev 116>> startxref 370428 %%EOF