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Eosinophilic esophagitis is an inflammatory condition, causing dysphagia, food impaction and chest pain. A minimum of 15 eosinophils per high power field by esophageal biopsy is necessary for diagnosis. It has become an increasingly important cause of gastrointestinal morbidity in the past two decades. A 14 year old boy had received a diagnosis of eosinophilic esophagitis elsewhere at the age of 8 years. His medical history had been thought for many years to be psychosomatic until endoscopy was performed. The only other positive laboratory study was eosinophilia. In spite of conventional therapy, none of which improved overall symptoms, esophagitis persisted and he had failed to gain weight and stature. Physical examination revealed many indications of autonomic dysfunction and an erythrocyte transketolase test indicated abnormal thiamine homeostasis. Treatment was started with intravenous infusions of water-soluble vitamins that included thiamine hydrochloride (THCL). Because the transketolase test became worse, THCL was replaced with thiamine tetrahydrofurfuryl disulfide (TTFD), with consequent improvement in transketolase and symptomatic response. There was a family history of alcoholism and the patient was addicted to sugar, suggesting a genetic risk to explain the abnormal thiamine homeostasis. Beriberi causes dysautonomia in its early stages. Inflammation is now known to be suppressed reflexly through the vagus nerve, itself dependent on acetylcholine. Abnormal motility of the esophagus has been reported in eosinophilic esophagitis. Failure of THCL to improve transketolase activity suggested a genetic failure in a thiamine transporter and its consequent correction with TTFD that does not require the thiamine transport system. © 2016 Lonsdale D. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Derrick Lonsdale* Eosinophilic Esophagitis Inflammation Thiamin homeostasis 2016-01-25T14:48:51+05:30 2016-01-25T14:48:52+05:30 2016-01-25T14:48:52+05:30 4 Adobe InDesign CS6 (Windows) uuid:6cc36882-f262-4a42-bafb-825a7617f43f xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 xmp.id:4F87139F44C3E51182CBF8D22AD9DDB5 proof:pdf xmp.iid:F07DB0C443C3E51182CBF8D22AD9DDB5 xmp.did:F2BC7D9EC6C7E411AEB789ACBE3823B3 xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 default converted from application/x-indesign to application/pdf Adobe InDesign CS6 (Windows) / 2016-01-25T14:48:51+05:30 Citation: Lonsdale D (2016) Is Eosinophilic Esophagitisa Sugar Sensitive Disease?. J Gastric Disord Ther 2(1): doi http://dx.doi.org/10.16966/2381-8689.114 Derrick Lonsdale, Associate Emeritus, Cleveland Clinic Foundation,Cleveland, Ohio, USA, E-mail: derricklonsdale@hotmail.com Adobe PDF Library 10.0.1 False endstream endobj 435 0 obj <> endobj xref 0 1729 0000000000 65535 f 0000237050 00000 n 0000237543 00000 n 0000237567 00000 n 0000245100 00000 n 0000245213 00000 n 0000245272 00000 n 0000245714 00000 n 0000245737 00000 n 0000245871 00000 n 0000255556 00000 n 0000255641 00000 n 0000255701 00000 n 0000256146 00000 n 0000257043 00000 n 0000257178 00000 n 0000266258 00000 n 0000266343 00000 n 0000266403 00000 n 0000266836 00000 n 0000267269 00000 n 0000267404 00000 n 0000271965 00000 n 0000272050 00000 n 0000272110 00000 n 0000272195 00000 n 0000272807 00000 n 0000273170 00000 n 0000273507 00000 n 0000274783 00000 n 0000290412 00000 n 0000290488 00000 n 0000291024 00000 n 0000291100 00000 n 0000291137 00000 n 0000327961 00000 n 0000328332 00000 n 0000328674 00000 n 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0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f 0000000000 65535 f trailer <<0B7556F2376C704999C967EF09F0C595>]>> startxref 116 %%EOF 434 0 obj <>stream application/pdf Is Eosinophilic Esophagitis a Sugar SensitiveDisease? Eosinophilic esophagitis is an inflammatory condition, causing dysphagia, food impaction and chest pain. A minimum of 15 eosinophils per high power field by esophageal biopsy is necessary for diagnosis. It has become an increasingly important cause of gastrointestinal morbidity in the past two decades. A 14 year old boy had received a diagnosis of eosinophilic esophagitis elsewhere at the age of 8 years. His medical history had been thought for many years to be psychosomatic until endoscopy was performed. The only other positive laboratory study was eosinophilia. In spite of conventional therapy, none of which improved overall symptoms, esophagitis persisted and he had failed to gain weight and stature. Physical examination revealed many indications of autonomic dysfunction and an erythrocyte transketolase test indicated abnormal thiamine homeostasis. Treatment was started with intravenous infusions of water-soluble vitamins that included thiamine hydrochloride (THCL). Because the transketolase test became worse, THCL was replaced with thiamine tetrahydrofurfuryl disulfide (TTFD), with consequent improvement in transketolase and symptomatic response. There was a family history of alcoholism and the patient was addicted to sugar, suggesting a genetic risk to explain the abnormal thiamine homeostasis. Beriberi causes dysautonomia in its early stages. Inflammation is now known to be suppressed reflexly through the vagus nerve, itself dependent on acetylcholine. Abnormal motility of the esophagus has been reported in eosinophilic esophagitis. Failure of THCL to improve transketolase activity suggested a genetic failure in a thiamine transporter and its consequent correction with TTFD that does not require the thiamine transport system. © 2016 Lonsdale D. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. Derrick Lonsdale* Eosinophilic Esophagitis Inflammation Thiamin homeostasis 2016-01-25T14:48:51+05:30 2016-01-25T14:48:58+05:30 2016-01-25T14:48:58+05:30 4 Adobe InDesign CS6 (Windows) uuid:82ce9194-40eb-45d9-9037-b2c46eb83a46 xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 xmp.id:4F87139F44C3E51182CBF8D22AD9DDB5 proof:pdf xmp.iid:F07DB0C443C3E51182CBF8D22AD9DDB5 xmp.did:F2BC7D9EC6C7E411AEB789ACBE3823B3 xmp.did:FE00469DB0C7E411AEB789ACBE3823B3 default converted from application/x-indesign to application/pdf Adobe InDesign CS6 (Windows) / 2016-01-25T14:48:51+05:30 Citation: Lonsdale D (2016) Is Eosinophilic Esophagitisa Sugar Sensitive Disease?. J Gastric Disord Ther 2(1): doi http://dx.doi.org/10.16966/2381-8689.114 Derrick Lonsdale, Associate Emeritus, Cleveland Clinic Foundation,Cleveland, Ohio, USA, E-mail: derricklonsdale@hotmail.com Adobe PDF Library 10.0.1 False endstream endobj 435 0 obj <> endobj 1730 0 obj <>/Metadata 434 0 R/Names 1731 0 R/Outlines 384 0 R/PageMode/UseOutlines/Pages 433 0 R/StructTreeRoot 436 0 R/Type/Catalog/ViewerPreferences<>>> endobj xref 0 1 0000000000 65535 f 434 2 0000439826 00000 n 0000447903 00000 n 1730 1 0000449971 00000 n trailer <<07893C2026C7CD418DDA87A555B7FFD1>]/Prev 116>> startxref 450175 %%EOF